Von Meyenburg Complexes or Biliary Hamartomas: A Case Report
DOI:
https://doi.org/10.52787/agl.v53i4.323Keywords:
Liver, bile ducts, Jaundice, intrahepatic cholestasisAbstract
Introduction. Von Meyenburg complexes or biliary hamartomas are a rare benign congenital anomaly of the intrahepatic bile ducts. They are usually asymptomatic and incidentally found on imaging studies but can cause jaundice, abdominal pain, and cholangitis.
Case report. An 80-year-old male patient was admitted to the emergency department due to progressive jaundice associated with pruritus, with an altered hepatogram and a cholestasis pattern. Imaging studies were performed in which there were no alterations in the liver parenchyma or bile ducts. A liver biopsy was performed, which revealed perivenular canalicular cholestasis and the presence of von Meyenburg complexes. The patient was treated with ursodeoxycholic acid with normalization of cholestasis at outpatient follow-up.
Conclusion. The diagnosis of biliary hamartomas should be considered in patients with intrahepatic cholestasis in whom the etiology is not identified by initial studies. They represent a diagnostic challenge as they are not always seen in imaging studies.
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